Description and Brand Names

Drug information provided by: IBM Micromedex

US Brand Name

  1. Carbaglu


Carglumic acid is used together with diet and other medicines to treat and prevent hyperammonemia (too much ammonia in the blood) when it is caused by the lack of a liver enzyme called N-acetylglutamate synthase (NAGS).

Ammonia is formed in the body when we digest protein. A person without the NAGS enzyme cannot process ammonia properly, and too much ammonia will collect in the blood. This will cause serious unwanted effects. Carglumic acid acts by replacing the NAGS enzyme and helps reduce the amount of ammonia in the blood.

This medicine is available only with your doctor's prescription.

This product is available in the following dosage forms:

  • Tablet