Double-outlet right ventricle

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Survival rates

With treatment, long-term survival is high for many children with DORV. Studies have reported survival rates above 85%.

There is no single survival rate for all types of DORV. The outlook depends on:

  • The structure of your child's heart.
  • The size of the ventricles and how well they work.
  • The type of DORV.
  • The type of repair.

Survival rates describe groups of people and cannot predict what may happen for one child.

In a study from Norway, 89.5% of children were alive five years after treatment. The same percentage of children were still alive 10 years after treatment.

In a 2025 study of 1,135 people who had surgery for DORV, 96.3% were alive at five years, 93% at 10 years and 92.7% at 15 years. The need for another surgery increased over time.

A 2024 study from several hospitals followed 81 children after a two-ventricle repair. At 10 years, 86% were alive. The outlook varied depending on the structure of the heart and how complex the repair was.

Talk with your child's care team about what the survival statistics mean for your child and what to expect over time.

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Diagnosis & treatment
Sept. 10, 2026

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  1. Xu Z, et al. Double outlet ventricles: Review of anatomic and imaging characteristics. Heart. 2023; doi:10.1136/heartjnl-2022-321955.
  2. Bell-Cheddar Y, et al. Double outlet right ventricle. Frontiers in Pediatrics. 2023; doi:10.3389/fped.2023.1244558.
  3. Holten-Andersen M, et al. Current outcomes of live-born children with double outlet right ventricle in Norway. European Journal of Cardio-Thoracic Surgery. 2023; doi:10.1093/ejcts/ezac560.
  4. Gurvitz M, et al. 2025 ACC/AHA/HRS/ISACHD/SCAI guideline for the management of adults with congenital heart disease: A report of the American College of Cardiology/American Heart Association Joint Committee on Clinical Practice Guidelines. Circulation. 2025; doi:10.1161/CIR.0000000000001402.
  5. Pang K, et al. Long-term surgical outcomes in double outlet right ventricle based on detailed anatomical sub-typology. European Journal of Cardio-Thoracic Surgery. 2025; doi:10.1093/ejcts/ezaf334.
  6. Rickert-Sperling S, et al., eds. Congenital Heart Diseases: The Broken Heart: Clinical Features, Human Genetics and Molecular Pathways. 2nd ed. Springer; 2024. https://link.springer.com/book/10.1007/978-3-031-44087-8. Accessed Aug. 17, 2026.
  7. Öcal A, et al. Navigating the spectrum of double-outlet right ventricle presentations: Outcomes from a contemporary cohort based on subtypes. Echocardiography. 2024; doi:10.1111/echo.15790.
  8. Moon-Grady AJ, et al. Guidelines and recommendations for performance of the fetal echocardiogram: An update from the American Society of Echocardiography. Journal of the American Society of Echocardiography. 2023; doi:10.1016/j.echo.2023.04.014.
  9. Pontailler M, et al. Long-term results after the réparation à l'étage ventriculaire procedure for transposition of the great arteries and double-outlet right ventricle with pulmonary stenosis. European Journal of Cardio-Thoracic Surgery. 2023; doi:10.1093/ejcts/ezad409.
  10. Lacour-Gayet F, et al. Multicentre study on late outcomes of biventricular repair of double outlet right ventricle. European Journal of Cardio-Thoracic Surgery. 2024; doi:10.1093/ejcts/ezad423.
  11. Medical review (expert opinion). Mayo Clinic. Sept. 3, 2026.

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Double-outlet right ventricle