概述

完全型肺静脉回流异常(TAPVR)是一种出生时即存在的罕见心脏状况。也就是说,它属于先天性心脏缺损。

该状况的其他名称为:

  • 完全型肺静脉连接异常。
  • TAPVC。

在这种心脏状况中,肺部血管(称为肺静脉)连接至心脏中错误的部位。

正常心脏中的富氧血从肺部流向心脏左上腔室(称为左心房),然后血液流向身体其他部位。

罹患 TAPVR 时,静脉连接会发生改变。血液流经右上心腔(称为右心房)。这种血流变化导致贫氧血与富氧血混合。这会导致流向身体的血液中氧气不足。

TAPVR 的类型取决于静脉连接的位置。大多数先天性 TAPVR 患儿没有先天性心脏病家族史。

Sept. 30, 2026

Living with 完全型肺静脉回流异常(TAPVR)?

Connect with others like you for support and answers to your questions in the Heart & Blood Health support group on Mayo Clinic Connect, a patient community.

Heart & Blood Health Discussions

sarah371
Brain MRI-small vessel brain disease & understanding findings

75 Replies Thu, Oct 29, 2026

pop77
Living with high calcium score

136 Replies Mon, Oct 12, 2026

See more discussions
  1. Total anomalous pulmonary venous connection (TAPVC). American Heart Association. https://www.heart.org/en/health-topics/congenital-heart-defects/about-congenital-heart-defects/total-anomalous-pulmonary-venous-connection-tapvc. Accessed Aug. 19, 2026.
  2. What is congenital heart disease? American Heart Association. https://www.heart.org/en/health-topics/congenital-heart-defects/about-congenital-heart-defects. Accessed Aug. 19, 2026.
  3. Soriano BD, et al. Total anomalous pulmonary venous connection. https://www.uptodate.com/contents/search. Accessed Aug. 19, 2026.
  4. Total anomalous pulmonary venous return (TAPVR). Centers for Disease Control and Prevention. https://www.cdc.gov/heart-defects/about/tapvr.html. Accessed Aug. 19, 2026.
  5. Martin RJ, et al., eds. Congenital defects of the cardiovascular system. In: Fanaroff and Martin's Neonatal-Perinatal Medicine: Diseases of the Fetus and Infant. 12th ed. Elsevier; 2025. https://www.clinicalkey.com. Accessed Aug. 24, 2024.
  6. Total anomalous pulmonary venous return (TAPVR). Merck Manual Professional Version. https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr. Accessed Aug. 19, 2026.
  7. Overview of congenital cardiovascular anomalies. Merck Manual Professional Version. https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/overview-of-congenital-cardiovascular-anomalies. Accessed Aug. 19, 2026.
  8. Congenital heart defects in children. Mayo Clinic. https://www.mayoclinic.org/diseases-conditions/congenital-heart-defects-children/symptoms-causes/syc-20350074. Accessed Aug. 19, 2026.
  9. Voleti SV, et al. Total anomalous pulmonary venous connections. Clinics in Perinatology. 2025; doi:10.1016/j.clp.2025.08.010.
  10. Stanley HM, et al. Multimodality imaging in presurgical evaluation of total anomalous pulmonary venous connection: Single-center practice variability and a systematic review of diagnostic error. Journal of the American Society of Echocardiography. 2025; doi:10.1016/j.echo.2025.05.020.
  11. Henningsen MB, et al. Nationwide registry study of long term survival and comorbidities in total anomalous pulmonary venous connection in Denmark. Scientific Reports. 2025; doi:10.1038/s41598-025-15769-0.