Diagnosis

Desmoplastic small round cell tumors are diagnosed with a procedure to remove a sample of cells for testing. This cancer happens when abnormal cells form in the soft tissues. It usually happens in the tissue that lines the inside of the belly. To remove the cells, you might need surgery or a needle can be passed through the skin. The cells are sent to a lab for testing. Imaging tests might also be needed, like ultrasound, CT, MRI, and PET.

Treatment

Surgery is usually used to treat desmoplastic small round cell tumors. This cancer happens when abnormal cells form in the soft tissues. It usually happens in the tissue that lines the inside of the belly. Surgeons work to remove as much of the cancer as they can. Other treatment options might include chemotherapy with strong drugs and radiation with powerful energy beams.

Desmoplastic small round cell tumors care at Mayo Clinic

Dec. 08, 2018
  1. Goldblum JR, et al. Malignant soft tissue tumors of an uncertain type. In: Enzinger and Weiss's Soft Tissue Tumors. 6th ed. Philadelphia, Pa.: Saunders Elsevier; 2014. http://www.clinicalkey.com. Accessed Jan. 31, 2017.
  2. Honore C, et al. Abdominal desmoplastic small round cell tumor: Multimodal treatment combining chemotherapy, surgery and radiotherapy is the best option. Annals of Surgical Oncology. 2015;22:1073.
  3. Jordan AH, et al. Management of desmoplastic small round-cell tumors in children and young adults. Journal of Pediatric Hematology/Oncology. 2012;34(suppl):S73.