Descripción general

El tumor desmoplásico de células pequeñas y redondas es un tipo de cáncer del tejido blando que, por lo general, comienza en el abdomen. En raras ocasiones, este tipo de cáncer puede ocurrir en otras partes del cuerpo.

El tumor desmoplásico de células pequeñas y redondas ocurre, con mayor frecuencia, en hombres jóvenes y niños varones, aunque puede aparecer a cualquier edad y también puede afectar a las mujeres.

Estos tipos de cáncer agresivos se forman, a menudo, como múltiples tumores en el tejido (peritoneo) que recubre el interior del abdomen y de la pelvis. Estos se propagan rápidamente a otras estructuras dentro del abdomen.

El tumor desmoplásico de células pequeñas y redondas es un tipo de sarcoma del tejido blando.

El tratamiento para los tumores desmoplásicos de células pequeñas y redondas consiste, generalmente, en una combinación de tratamientos, como la cirugía, la quimioterapia y la radioterapia.

Síntomas

Desmoplastic small round cell tumor symptoms vary depending on where the cancer begins. Most often it begins in the abdomen.

Signs and symptoms of desmoplastic small round cell tumors in the abdomen include:

  • Swelling of the abdomen
  • Abdominal pain
  • Constipation
  • Difficulty urinating

When to see a doctor

Make an appointment with your health care provider if you have any persistent signs and symptoms that worry you.

Causas

It's not clear what causes desmoplastic small round cell tumors.

Doctors know that cancer begins when a cell develops changes in its DNA. A cell's DNA contains the instructions that tell a cell what to do. The changes tell the cell to multiply quickly. This creates a clump of cancer cells called a tumor. The cancer cells can invade and destroy healthy body tissue. In time, the cancer cells can break away and spread to other parts of the body.

Tumores desmoplásicos de células pequeñas y redondas - atención en Mayo Clinic

June 01, 2022
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