概述

结缔组织增生性小圆细胞肿瘤是一种软组织癌,通常发生在腹部。但在极少数情况下,这种癌症可发生在身体其他部位。

结缔组织增生性小圆细胞肿瘤最常发生在年轻男性和男孩中,但任何年龄段均可发生,也可能累及女性。

这些侵袭性癌症通常在腹部和骨盆内衬组织(腹膜)中形成多发性肿瘤。它们会迅速扩散到腹部的其他结构。

结缔组织增生性小圆细胞肿瘤是一种软组织肉瘤。

结缔组织增生性小圆细胞肿瘤的治疗通常包括手术、化疗和放射疗法等联合治疗。

症状

Desmoplastic small round cell tumor symptoms vary depending on where the cancer begins. Most often it begins in the abdomen.

Signs and symptoms of desmoplastic small round cell tumors in the abdomen include:

  • Swelling of the abdomen
  • Abdominal pain
  • Constipation
  • Difficulty urinating

When to see a doctor

Make an appointment with your health care provider if you have any persistent signs and symptoms that worry you.

病因

It's not clear what causes desmoplastic small round cell tumors.

Doctors know that cancer begins when a cell develops changes in its DNA. A cell's DNA contains the instructions that tell a cell what to do. The changes tell the cell to multiply quickly. This creates a clump of cancer cells called a tumor. The cancer cells can invade and destroy healthy body tissue. In time, the cancer cells can break away and spread to other parts of the body.

在 Mayo Clinic 治疗

June 01, 2022

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  6. Chicago Consensus Working Group. The Chicago consensus of peritoneal surface malignancies: Management of desmoplastic small round cell tumor, breast and gastrointestinal stromal tumors. Cancer. 2020; doi:10.1002/cncr.32856.