Description and Brand Names

Drug information provided by: Merative, Micromedex®

US Brand Name

  1. Kalydeco


Ivacaftor is used to treat cystic fibrosis (CF). It is only used for patients who have the following mutations in their CF transmembrane conductance regulator (CFTR) gene: G551D, G1244E, G1349D, G178R, G551S, R117H, S1251N, S1255P, S549N, or S549R mutations. Your doctor will test for the presence of the mutation before you receive the medicine. Ivacaftor is a CFTR potentiator, and works by moving more chloride into the cells of your body.

This medicine is available only with your doctor's prescription.

This product is available in the following dosage forms:

  • Tablet
  • Granule