完全型肺静脉回流异常(TAPVR) 概述

完全型肺静脉回流异常(TAPVR)是一种出生时即存在的罕见心脏状况。也就是说,它属于先天性心脏缺损。

该状况的其他名称为:

  • 完全型肺静脉连接异常。
  • TAPVC。

在这种心脏状况中,肺部血管(称为肺静脉)连接至心脏中错误的部位。

正常心脏中的富氧血从肺部流向心脏左上腔室(称为左心房),然后血液流向身体其他部位。

罹患 TAPVR 时,静脉连接会发生改变。血液流经右上心腔(称为右心房)。这种血流变化导致贫氧血与富氧血混合。这会导致流向身体的血液中氧气不足。

TAPVR 的类型取决于静脉连接的位置。大多数先天性 TAPVR 患儿没有先天性心脏病家族史。

Dec. 07, 2024

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