多发性内分泌腺瘤病 1 型 (MEN 1)

概述

多发性内分泌腺瘤病 1 型（MEN 1）有时也称为 Wermer 综合征，这种罕见的疾病会导致内分泌腺以及小肠和胃的某些部分出现肿瘤。在多发性内分泌腺瘤病 1 型中，内分泌腺（通常是副甲状腺、胰腺和垂体）会长出肿瘤，并释放可能引起疾病的过量激素。但是，这些肿瘤通常是非癌性（良性）的。

过量的激素可能引起各种体征和症状，其中包括疲劳、骨痛、骨折、肾结石以及胃或肠溃疡。MEN 1 尚无治愈方法，但定期接受检测可以发现问题，医生可以根据需要提供治疗。

MEN 1 是一种遗传性疾病，这意味着出现基因突变的人可能将这种疾病遗传给他们的子女。每个子女都有 50% 的几率遗传这种疾病。

MEN 1 的体征和症状包括：

导致这些症状的原因是体内激素分泌过多。

Aug. 31, 2022

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