Urine odor is related to the volume and concentration of a variety of substances excreted by the kidneys. Normally, urine that contains a lot of water has little to no odor. If your urine becomes highly concentrated — a high level of waste products with little water — urine odor may have a strong ammonia smell.

Many foods and medications, such as asparagus or certain vitamins, can affect the odor of urine. Sometimes, unusual urine odor may indicate a medical condition or disease, such as:

  1. Bladder infection
  2. Cystitis (bladder inflammation)
  3. Congenital heart disease in adults
  4. Diabetic ketoacidosis (high levels of blood acids called ketones)
  5. Gastrointestinal-bladder fistula (abnormal connection between the intestines and bladder)
  6. Maple syrup urine disease (rare genetic disease that causes difficulty breaking down certain amino acids)
  7. Metabolic disorder (a problem with the way your body converts the foods you eat into energy)
  8. Type 2 diabetes (uncontrolled)
  9. Urinary tract infection (UTI)

Causes shown here are commonly associated with this symptom. Work with your doctor or other health care professional for an accurate diagnosis.

April 23, 2014