Ehlers-Danlos Syndrome

Types

Ehlers-Danlos syndrome can be categorized into six major types. Most types affect the joints and skin; the vascular type affects the blood vessels and internal organs. Your type is classified according to your signs and symptoms.

Classical

• Skin can stretch beyond normal range (hyperextensibility)
• Widened thin scars
• Joint flexibility (hypermobility)

Hypermobility

• Generalized joint hypermobility
• Stretchy skin
• Smooth or velvety skin

Vascular

• Fragile arteries, intestines or uterus subject to sudden rupturing
• Thin, translucent skin
• Easy bruising
• Characteristic facial features

Kyphoscoliotic

• Joint looseness
• Severe muscle weakness (hypotonia)
• Curving of the spine (scoliosis)
• Fragile white part (sclera) of eye

Arthrochalasia

• Hip dislocation from birth (congenital)
• Severe joint hypermobility with dislocations

Dermatosparaxis

• Severe skin fragility
• Soft, doughy and saggy skin