Ebstein's anomaly is a rare heart defect that's present at birth (congenital). In Ebstein's anomaly, your tricuspid valve — the valve between the two right heart chambers (right atrium and right ventricle) — doesn't work properly. The tricuspid valve sits lower than normal in the right ventricle, and the tricuspid valve's leaflets are abnormally formed.
Blood may leak back through the valve, making your heart work less efficiently. Ebstein's anomaly may also lead to enlargement of the heart or heart failure.
If you have no signs or symptoms associated with Ebstein's anomaly, careful monitoring of your heart may be all that's necessary. If signs and symptoms bother you, or if the heart is enlarging or becoming weaker, treatment for Ebstein's anomaly may be necessary. Treatment options include medications and surgery.
Ebstein's anomaly care at Mayo Clinic
March 28, 2017
- Ebstein's anomaly. American Heart Association. http://www.heart.org/HEARTORG/Conditions/CongenitalHeartDefects/AboutCongenitalHeartDefects/Ebsteins-Anomaly_UCM_307025_Article.jsp#.VqE5kdhIjmI. Accessed Jan. 11, 2016.
- Fuster V, et al., eds. Congenital heart disease in children and adolescents. In: Hurst's The Heart. 13th ed. New York, N.Y.: The McGraw-Hill Companies; 2011. http://www.accessmedicine.com. Accessed Jan. 11, 2016.
- Agarwala BN, et al. Ebstein's anomaly of the tricuspid valve. http://www.uptodate.com/home. Accessed Jan. 11, 2016.
- What are congenital heart defects? National Heart, Lung, and Blood Institute. http://www.nhlbi.nih.gov/health/health-topics/topics/chd. Accessed Jan. 14, 2016.
- Patent foramen ovale (PFO). American Heart Association. http://www.heart.org/HEARTORG/Conditions/More/CardiovascularConditionsofChildhood/Patent-Foramen-Ovale-PFO_UCM_469590_Article.jsp#.VqE7jdhIjmI. Accessed Jan. 15, 2016.
- Crawford MH. Congenital heart disease in adults. In: Current Diagnosis & Treatment: Cardiology. 4th ed. New York, N.Y.: The McGraw-Hill Companies; 2014. http://www.accessmedicine.com. Accessed Jan. 11, 2016.
- Katsuragi S, et al. Risk factors for maternal and fetal outcome in pregnancy complicated by Ebstein anomaly. American Journal of Obstetrics and Gynecology. 2013;209:452.e1.
- What is an arrhythmia? National Heart, Lung, and Blood Institute. http://www.nhlbi.nih.gov/health/health-topics/topics/arr. Accessed Jan. 18, 2016.
- Dearani JA, et al. Strategies for tricuspid re-repair in Ebstein malformation using the cone technique. The Annals of Thoracic Surgery. 2013;96:202.
- Anderson HN, et al. Cone reconstruction in children with Ebstein anomaly: The Mayo Clinic experience. Congenital Heart Disease. 2014;9:266.
- Brown ML, et al. The outcomes of operations for 539 patients with Ebstein anomaly. The Journal of Thoracic and Cardiovascular Surgery. 2008;135:1120.
- Dearani JA, et al. Ebstein anomaly review: What's now, what's next? Expert Review of Cardiovascular Therapy. 2015;13:1101.
- Getting support. American Heart Association. http://www.heart.org/HEARTORG/Caregiver/ReachOut/GettingSupport/Getting-Support_UCM_301847_Article.jsp#.VqE-u9hIjmI. Accessed Jan. 19, 2016.
- Finding support. Centers for Disease Control and Prevention. http://www.cdc.gov/ncbddd/birthdefects/families-support.html. Accessed Jan. 19, 2016.
- Riggin EA. Decision Support System. Mayo Clinic, Rochester, Minn. Jan. 14, 2016.